本文报道1例诊断为肝豆状核变性，头颅MRI影像表现为脑桥“小熊猫脸征”的患者，通过回顾肝豆状核变性众多特殊神经影像征的发现历程以及病理生理学机制，探讨肝豆状核变性的特殊影像学的诊断以及鉴别。

This article reports a case diagnosed as hepatolenticular degeneration, with cranial MRI images suggesting the "face of the panda cub" in the pontine tegmentum. By reviewing the discovery process and pathophysiological mechanisms of numerous special neuroimaging signs of hepatolenticular degeneration, we trend to explore the special imaging diagnosis and differential diagnosis of hepatolenticular degeneration.